Ivacaftor in cystic fibrosis with residual function: Lung function results from an N-of-1 study
نویسندگان
چکیده
منابع مشابه
Lung function in infants with cystic fibrosis.
Lung function was measured in 28 infants with cystic fibrosis and repeated in 17 of the infants during the first year of life. Thoracic gas volume (TGV) and specific airway conductance (sGaw) were measured plethysmographically and maximum forced expiratory flow at functional residual capacity (VmaxFRC) was derived from the partial expiratory flow-volume curve. At the time of the initial evaluat...
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translation as a comunicative process is always said to be associated with various aspects of meaning loss or gain. subtitling as a mode of translating, due to special discoursal and textual conditions imposed upon it, is believed to be an obvious case of this loss or gain. presenting the spoken sound track of a film in writing and synchronizing the perception of this text by the viewers with...
15 صفحه اولLung function from infancy to school age in cystic fibrosis.
The aim was to investigate pulmonary mechanics in patients with cystic fibrosis during infancy and again in early childhood to see whether infant tests predicted status at school age. Plethysmographic measurements of thoracic gas volume and airways resistance were made in 29 patients at 6 months and again at 5 years 10 months. Maximum flow at functional residual capacity was measured during inf...
متن کاملGrowth and lung function in Asian patients with cystic fibrosis.
BACKGROUND The incidence of cystic fibrosis (CF) in Asians is rare. How these patients fare in terms of morbidity and mortality in the UK compared to their non-Asian peers is not well documented. AIMS To retrospectively study annual reviews of 31 Asian CF patients from three London paediatric CF centres. METHODS Disease severity was assessed by lung function, age at first infection with Pse...
متن کاملPredictors of deterioration of lung function in cystic fibrosis.
The severity of lung disease in cystic fibrosis (CF) may be related to the type of mutation in the cystic fibrosis transmembrane conductance regulator (CFTR) gene, and to environmental and immunological factors. Since pulmonary disease is the main determinant of morbidity and mortality in CF, it is important to identify factors that can explain and predict this variation. The aim of this longit...
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ژورنال
عنوان ژورنال: Journal of Cystic Fibrosis
سال: 2020
ISSN: 1569-1993
DOI: 10.1016/j.jcf.2019.09.013